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(ARACHNODACTYLY COUPLED WITH DISLOCATION OF THE LENS)

ANDREW RADOS, M.D.

Arch Ophthal. 1942;27(3):477-538.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

Recognition of the association between ocular manifestations and pathologic changes as well as malformations in distant parts of the body belongs to one of the fastest growing chapters in ophthalmologic knowledge. Ocular changes accompanying osseous dystrophies form well circumscribed entities. Optic nerve atrophy in oxycephaly, exophthalmos and ophthalmoplegias in Apert's syndrome (acrocephalysyndactyly), optic nerve atrophy in dystrophia craniofacialis (Crouzon), optic nerve atrophy and divergent strabismus with synostosis of the major and minor alae of the sphenoid bone, blue sclera, deafness and osteoporosis causing spontaneous fractures (Lobstein's disease) are but a few illusstrations. In another group of ocular changes, linkage with anomalies of the fingers is characteristic. Retinitis pigmentosa occurs with polydactyly, microcornea with brachydactyly, aniridia with dystrophy of the hands and feet or with malformation of the hands in the form of des pinces de homard and, finally, congenital dislocation of the lenses with arachnodactyly (Marfan's syndrome). The exact clinical . . . [Full Text PDF of this Article]

Author Affiliations
NEWARK, N. J.

From the Ophthalmic Department of the Beth Israel Hospital.

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