This Article  • References  • Full text PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Citing articles on Web of Science (6)  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

John I. Loewenstein, MD
Boston, Mass

Arch Ophthalmol. 1995;113(2):143-144.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

von Hippel-Lindau disease is a member of the group of phakomatoses. It is characterized by formation of angiomas or hemangioblastomas in the retina, cerebellum, and occasionally in other tissues. Pheochromocytoma and renal cell carcinoma may also occur. Polycythemia can be seen, usually with cerebellar hemangioblastomas, renal cell carcinomas, or pheochromocytomas.¹

The retinal tumors usually enlarge, and exudation from these lesions may lead to retinal detachment. Less commonly, peripheral retinal breaks may occur, leading to rhegmatogenous detachment.² This may occur after treatment of an angioma.

I have observed a case with several unusual features. Preretinal membranes were present in both eyes, with spontaneous peeling in one eye and peeling after treatment of a peripheral angioma in the other eye. In both eyes, macular breaks resulted. In the treated eye, rhegmatogenous detachment occurred as a result of the macular break, along with traction originating from the treated lesion. The patient . . . [Full Text PDF of this Article]

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?