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Syril K. Dorairaj, MD; Alan Robin, MD; Wisam Shihadeh, MD; Steven Greenberg, MD; Jeffrey M. Liebmann, MD; Robert Ritch, MD

Arch Ophthalmol. 2007;125(1):136-138.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Pigment dispersion syndrome (PDS) typically develops in young adults and is most commonly diagnosed in the third and fourth decades, although the mean age at onset remains unknown.¹ The diagnostic triad of PDS consists of Krukenberg spindle on corneal endothelium, slitlike, radial, midperipheral iris transillumination defects, and dense, homogeneous trabecular meshwork pigmentation.¹ Pigment dispersion syndrome is rarely seen before the midteenaged years. Grassi et al² described atypical pigment dispersion in an 8-year-old boy. We describe an 11-year-old girl with bilateral PDS with elevated intraocular pressure (IOP) as well as two 12-year-old boys, one with a more severe phenotype and both parents affected (suggesting the probability of homozygosity or inheritance of a predisposing gene from each parent) and the other with a less severe phenotype and 1 parent affected (showing the . . . [Full Text of this Article]

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