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Arch Ophthalmol. 2005;123:565-567.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Desmoplastic small round cell tumor (DSRCT) is an uncommon yet potentially lethal tumor typically affecting young male adults. This extremely aggressive tumor was first described by Gerald and Rosai¹ in 1989, and since then, more than 250 cases have been reported,² with recent cytogenetic work revealing a unique translocation involving the Ewing sarcoma breakpoint region (EWSR1) at t(11;22)(p13;q12). In the largest case report to date, 94% of 109 cases were located in the abdominal cavity.³ Other serosal surfaces may be involved, including the testis, ovary, pleura, and parotid gland.⁴ Manifestations in the head are extremely uncommon. Desmoplastic small round cell tumor has been reported once in the ethmoidal sinuses⁵ and once in the posterior cranial fossa.⁶ The current report describes the first patient, to our knowledge, with DSRCT producing visual disturbances as an initial complaint.

Report of a Case

A 32-year-old man was in his usual state of health when he saw his physician . . . [Full Text of this Article]

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AUTHOR INFORMATION
Michael Yoon, BSc; Komal Desai, MD; Regan Fulton, MD, PhD; Kara Bucci, MD; Michael Russin, MD; R. Max. Conway, MD, PhD; Joan M. O’Brien, MD