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Arch Ophthalmol. 2005;123:1443-1445.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Localized neurofibromas are rare in the orbit and, unlike plexiform neurofibromas, are not typically associated with von Recklinghausen neurofibromatosis. To our knowledge, bilaterality of such localized neurofibromas has been reported only once.¹ We report a patient known to have Charcot-Marie-Tooth disease (CMTD) who developed multiple localized neurofibromas in both orbits.

Report of a Case

A 35-year-old man, known to have CMTD polyneuropathy since the age of 12 years, was referred to us because of the accidental finding of bilateral orbital tumors on magnetic resonance imaging of the brain. The brain imaging had been requested by a neurologist after the patient developed a right-sided trigeminal neuralgia.

On evaluation, bilateral exophthalmos was noted, and this was reported by the patient to be of long-standing duration (at least 5 years). Best-corrected visual acuity was 20/30 in either eye. Hertel exophthalmometry measurements were 23 mm in both eyes. There was mild limitation of supraduction in both eyes. Tonic . . . [Full Text of this Article]

Pathologic Findings

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AUTHOR INFORMATION
Riad N. Ma’luf, MD; Baha’ N. Noureddin, MD; Nicola G. Ghazi, MD; Ayman N. Tawil, MD; Suha S. Allam, MD