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Arch Ophthalmol. 2003;121:1053-1054.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Bilateral infantile corneal opacities can be caused by anterior segment dysgenesis, corneal dystrophy, congenital glaucoma, inflammation, systemic storage disease, or sclerocornea.^1-5 We describe a mother and son with bilateral superior V-shaped corneal opacities, cornea guttata, and corectopia. This unique combination of anterior segment abnormalities has not, to our knowledge, been reported to be inherited.

Report of Cases

Case 1

A 14-day-old term male infant had bilateral congenital corneal opacities. He could not fix or follow a light source. Slitlamp examination showed dense bilateral superior V-shaped corneal opacities (Figure 1). In the area of opacification, there were a few iridocorneal adhesions and what appeared to be cornea guttata in both eyes. The pupil was drawn superiorly and was occluded by the corneal opacities in both eyes. The lens and fundus could not be visualized. There were no signs of inflammation, systemic dysmorphism, or an intrauterine-derived infection. Preoperative ultrasonography revealed a normal lens and vitreous . . . [Full Text of this Article]

Case 2

Comment
Corresponding author and reprints: Elias I. Traboulsi, MD, Center for Genetic Eye Disease, Cole Eye Institute, the Cleveland Clinic Foundation, i32, 9500 Euclid Ave, Cleveland, OH 44195 (e-mail: traboue@ccf.org).