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Arch Ophthalmol. 2003;121:1047-1049.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

X-linked lymphoproliferative disorder (XLPD) is a hereditary disease that stems from a deletion Xq 23-25 that negates the functions of an immune response to the Epstein-Barr virus (EBV). Males who inherit the mutation develop a spectrum of conditions that include fatal infectious mononucleosis, hypogammaglobulinemia, B-cell lymphomas in extranodal sites, and aplastic anemia after EBV infection.¹ Although the virus has previously been implicated in chorioretinitis and retinal vasculitis in patients with infectious mononucleosis,² to our knowledge there is only 1 report in the literature of retinal necrosis associated with XLPD.³ Herein we present the case of a 10-month-old boy with XLPD and pathologically confirmed retinal necrosis.

Report of a Case

A 10-month-old boy was referred for a dilated fundus examination prior to bone marrow transplantation for aplastic anemia secondary to XLPD. The patient's serologic test results were positive for EBV, cytomegalovirus (CMV), and herpes simplex virus (HSV). He was able to fix and follow with . . . [Full Text of this Article]

Comment
Corresponding author and reprints: Robert K. Hutchins, MD, 3219 Clifton Ave, Suite 210, Cincinnati, OH 45242 (e-mail: retinainc@msn.com).