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Arch Ophthalmol. 2003;121:727-729.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Klippel-Trénaunay syndrome (KTS) is a congenital vascular anomaly with soft tissue and skeletal hypertrophy. It has been associated with capillary, venous, lymphatic, and soft tissue malformations, but not with malignancies. Orbital rhabdomyosarcoma typically demonstrates a rapid-onset orbital process that can be confused with trauma or benign tumors. This case report underscores that rhabdomyosarcoma can mimic a benign, lymphatic malformation, particularly in the setting of expected vascular lesions. A comprehensive MEDLINE search failed to identify a previous case of concurrent KTS and orbital rhabdomyosarcoma. Current chemotherapeutic regimens are reviewed.

Report of a Case

A 3-year-old boy had an inferonasal conjunctival mass of 10 days' duration and a recent upper respiratory tract infection (URTI), including nasal congestion, rhinorrhea, and epiphora. Examination revealed a right, vascular conjunctival mass (Figure 1) and a grade 1 port-wine stain¹ (diffuse capillary and venular malformation) of the left upper extremity (Figure 2A), with soft tissue hypertrophy of . . . [Full Text of this Article]

Comment
Corresponding author and reprints: Aaron Fay, MD, 243 Charles St, Boston, MA 02114 (e-mail: aaron_fay@meei.harvard.edu).

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