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Arch Ophthalmol. 2002;120:653-655.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

INTRODUCTION

Malignant peripheral nerve sheath tumor (MPNST) is an extremely rare orbital tumor and only 34 cases have previously been reported^1-10 Of these, only 5 were childhood cases of MPNST occurring in the orbit.^3-4,7-9 We report a sixth case of this disease in the orbit of an 11-year-old girl who had rapidly progressive proptosis and optic nerve compression.

Report of a Case

An 11-year-old girl was referred with a 5-day history of rapidly progressive painless proptosis of the left eye and a corrected visual acuity that had decreased from 6/5 to 6/12 over the previous 24 hours. On examination, the left eye was noted to have a 5-mm axial proptosis with a relative afferent pupillary defect and a swollen optic disc. Ocular motility was unrestricted and she did not complain of diplopia. There was no palpable periorbital mass and no periorbital neurosensory deficit. She was otherwise healthy with no significant medical history. A magnetic resonance . . . [Full Text of this Article]

Comment

Corresponding author: B. Leatherbarrow, FRCS, FRCOphth, Royal Eye Hospital, Oxford Road, Manchester M13 9WH, England (e-mail: bollin@mighty-micro.co.uk).