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Arch Ophthalmol. 1998;116:682-684.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Incontinentia pigmenti is a rare X-linked disorder that affects the eyes, central nervous system, skin, and teeth.^1-2 Ocular abnormalities are seen in approximately 35% of patients³ and include conjunctival pigmentation, strabismus, cataracts, optic atrophy, and retinal abnormalities.² The main retinal findings include macular capillary dropout, peripheral avascularity, arteriovenous anastomoses at the junction of the vascular and avascular retina, preretinal neovascularization, and retinal detachment.¹ We now report 2 cases of persistence of fetal vasculature (PFV) in the eyes of patients with incontinentia pigmenti.

Report of Cases

Case 1

An 8-month-old female infant was referred from the Department of Dermatology with the diagnosis of incontinentia pigmenti having been made 1 month prior to our initial examination. The family history was unremarkable. She was the product of a full-term vaginal delivery and had no neonatal oxygen therapy. She was healthy except for the presence of an erythematous vesicular rash since birth. An irregular pupil had been noted in . . . [Full Text of this Article]

Case 2

Comment
Reprints: Morton F. Goldberg, MD, 727 Maumenee Bldg, 600 N Wolfe St, Baltimore, MD 21287.

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Novel corneal features in two males with incontinentia pigmenti
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Br. J. Ophthalmol. 2003;87:554-556.
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