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Arch Ophthalmol. 1998;116:383-385.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

In 1952, Wildervanck¹ described a cervico-oculo-acoustic syndrome consisting of Klippel-Feil deformity, abducens palsy with globe retraction, and congenital hearing loss. Subsequent reports have confirmed that the Wildervanck syndrome occurs sporadically, preferentially affects girls, and may be associated with paralysis of other lower cranial nerves.² We describe a posterior fossa malformation complex with hypoplasia of the brainstem that was demonstrated by magnetic resonance imaging in a child with Wildervanck syndrome.

Report of a Case

A 5-month-old girl was referred to us for evaluation of intermittent esotropia. She was born at 37 weeks gestational age and weighed 2.2 kg at birth. A maternal great-grandfather had a history of Sprengel deformity (congenital elevation of the scapula), but a fraternal twin and 2 older sisters had no malformations. The findings of a facial examination included esotropia, diminished lower facial tone, low-set ears, and bilateral hearing aids (Figure 1, A). Skeletal abnormalities included thoracic kyphosis; a webbed, . . . [Full Text of this Article]

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Reprints: Michael C. Brodsky, MD, Arkansas Children's Hospital, 800 Marshall, Little Rock, AR 72202.

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