Electrophysiologic findings in bilateral optic nerve hypoplasia
J. B. Sprague and W. B. Wilson
Electrophysiologic studies were performed on 17 patients with bilateral
optic nerve hypoplasia. Since most patients were infants, the diffuse light
visual-evoked response was more helpful than the visual-evoked response
obtained with pattern stimulation. In children over 1 year of age, the
amplitude with diffuse light stimulation correlated well with other
clinical measurements used to assess visual function. Before 6 months of
age, it correlated better with visual prognosis than did clinical analysis.
Photopic and scotopic electroretinographic measurements were normal in all
except two in whom the scotopic b wave was supernormal.