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Ocular Pathology of the Batten-Vogt Syndrome

Sydney S. Schochet, Jr, MD; Ramon L. Font, MD; Harold H. Morris III, MD

Arch Ophthalmol. 1980;98(6):1083-1088.

Abstract
• The neuronal ceroid-lipofuscinoses (Batten-Vogt syndrome) are a group of at least four closely related entities that are characterized by the accumulation of autofluorescent lipopigments in neural, visceral, and somatic tissues. The ophthalmic pathology of this syndrome has been investigated less extensively than other tissues and organs. In this report, we present the postmortem ocular findings, including light, fluorescence, and electron microscopy, from a child with the Jansky-Bielschowsky form of this syndrome.

Author Affiliations
From the Departments of Pathology (Neuropathology) (Dr Schochet) and Neurology (Dr Morris), University of Texas Medical Branch, Galveston, and Department of Ophthalmic Pathology, Armed Forces Institute of Pathology, Washington, DC (Dr Font). Dr Font is now with the Cullen Eye Institute, Houston.

Footnotes
Accepted for publication Dec 4, 1979.

The opinions or assertions contained herein are the private views of the authors and are not to be construed as official or as reflecting the views of the Department of the Army or the Department of Defense.

Reprint requests to Laboratory of Ophthalmic Pathology, Cullen Eye Institute, Baylor College of Medicine, Houston, TX 77030 (Dr Font).

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