Juvenile fibromatosis of the periorbital region and eyelid. A clinicopathologic study of six cases
A. A. Hidayat and R. L. Font
Six cases of juvenile fibromatosis of the periorbital region and eyelid
were studied. The median age of the patients was 8 years (range, 1 to 11
years). A definite propensity for involvement of the infraorbital region
and lower eyelid was observed. THREE TUMORS EXHIBITED A PROMINENT LOBULAR
PATTERN AND WERE ADHERENT TO THE PERIOSTEUM. The main entities in the
differential diagnosis included leiomyoma, neurofibroma, and
well-differentiated fibrosarcoma. Two of six tumors recurred locally but
did not metastasize. Electron microscopic studies disclosed that the
spindle-shaped tumor cells exhibited features of fibroblasts. It appears
that conservative treatment (ie, local excision) is adequate.
