Cafe-au-lait spots of the fundus in neurofibromatosis
E. Cotlier
Mild pigmentary changes found in the fundi of two patients with
neurofibromatosis, resembled cafe-au-lait spots homologous with skin
manifestations of the disease. In one, associated retinal hamartomas were
present. The cafe-au-lait lesions were clinically distinct from previously
reported uveal melanomas and may represent a hitherto unrecognized sign of
ocular neurofibromatosis.
