Paradoxical pupillary responses in congenital stationary night blindness
M. E. Barricks, J. T. Flynn and B. J. Kushner
Three unrelated boys, ages 2, 6, and 10 years, who have congenital
stationary night blindness with myopia and a Schubert-Bornschein-type
electroretinogram finding, were found to show a "paradoxical" pupillary
constriction in darkness. When examining room lights are turned out, the
patient's pupils briskly constrict and slowly dilate. Older night blind
male relatives of these boys did not show this abnormal constriction to
darkness.