Olivopontocerebellar degeneration. Clinicopathologic correlation of the associated retinopathy
S. J. Ryan Jr, D. L. Knox, W. R. Green and B. W. Konigsmark
In two siblings with olivopontocerebellar degeneration, the retinal pigment
epithelium or the sensory retinal or both appeared to be damaged first.
These layers were markedly involved before secondary changes in the
choriocapillaris, the inner retinal layers, or the optic nerve occurred.