Simple choristoma of the anterior segment containing brain tissue
W. E. Marshman, C. J. Lyons, D. W. Young and V. A. White
Department of Ophthalmology, British Columbia's Children's Hospital, Vancouver.
We report an unusual case of a simple choristoma of the anterior segment
that contained only brain tissue. The clinical characteristics and findings
of pathological examination of this unusual ocular malformation were
reviewed. A newborn girl was seen with a fleshy, highly vascular cystic
mass arising from the inferior limbus and extending across the cornea. On a
computed tomographic scan, gross disruption of the anterior segment was
present, with subluxation of the lens into the cyst. Excision of the
abnormal tissue was followed by evisceration; polyglactin (Vicryl) ball
implantation; patch graft of the globe; and, later, prosthetic fitting.
Pathologic findings showed a choristomatous malformation, containing only
mature brain tissue. To our knowledge, a choristoma in which the sole
constituent is brain tissue has not previously been reported.
