Periorbital infantile myofibromatosis
J. S. Linder, G. J. Harris and A. D. Segura
Department of Ophthalmology, Medical College of Wisconsin, Milwaukee, USA.
An 11-day-old boy was found to have a lesion of the left lower eyelid and
medial canthus. The mass was present at birth and subsequently enlarged,
and was subtotally excised when the child was 2 months old. Histopathologic
examination disclosed a fascicular to slightly nodular pattern of
predominantly spindle-shaped cells. Special stains demonstrated
fibroblastic and smooth-muscle features in individual cells, and infantile
myofibromatosis was diagnosed. Sixteen months postoperatively, no evidence
of recurrence was noted. We believe this is the first case of infantile
myofibromatosis of the solitary type involving the ocular adnexa of a
neonate to be reported in the English literature. Infantile myofibromatosis
of the solitary type appears to have an excellent prognosis and may be
treated with conservative resection if the tumor infiltrates important
adnexal structures.
