Retinal detachments in incontinentia pigmenti
K. J. Wald, M. C. Mehta, O. Katsumi, N. R. Sabates and T. Hirose
Retina Associates, Schepens Eye Research Institute, Harvard Medical School, Boston, Mass 02114.
We report on retinal detachments in six eyes of four patients with
incontinentia pigmenti. These nonrhegmatogenous traction retinal
detachments are characterized by extensive preretinal and vitreous fibrous
organization that pull the retina anteriorly behind the lens. The clinical
course and fundus appearance of the retinal detachments, beginning with the
avascular peripheral retina and leading to traction retinal detachment, are
similar to those of cicatricial retinopathy of prematurity. Vitreous
surgery was performed on three eyes (two patients), with partial
reattachment of a total retinal detachment in one eye and complete
reattachment of a partial retinal detachment in a second eye. These cases
represent the first successful surgical interventions reported for retinal
detachment in incontinentia pigmenti.
