Poorly differentiated primary orbital sarcoma (presumed malignant rhabdoid tumor). Radiologic and histopathologic correlation
L. N. Johnson, F. M. Sexton and S. H. Goldberg
Neuro-Ophthalmology Division, Mason Institute of Ophthalmology, University of Missouri-Columbia 65212.
A 47-year-old man presented with acquired hyperopia and gaze-evoked visual
loss. Computed tomography and magnetic resonance imaging demonstrated a
well-circumscribed intraconal tumor. Histopathologic studies indicated that
the tumor was a poorly differentiated primary orbital sarcoma compatible
with malignant fibrous histiocytoma or malignant rhabdoid tumor. To our
knowledge, no case of primary orbital malignant rhabdoid tumor has been
previously described in an adult.
