Corneal choristoma with microphthalmos
T. Murata, T. Ishibashi, Y. Ohnishi and H. Inomata
Department of Ophthalmology, Faculty of Medicine, Kyushu University, Fukuoka, Japan.
We report two rare cases of corneal choristoma with microphthalmos. In both
cases, the whole thickness of the cornea, as well as the anterior chamber
and iris, was replaced by cutaneous and subcutaneous tissue. In case 1,
diagnosed as dermoid choristoma, the cutaneous tissue contained skin
appendages and subcutaneous fibrofatty tissue extended into the vitreous
cavity. The fibrous mass in the cavity contained fragments of retina. In
case 2, diagnosed as a dermislike choristoma, the cutaneous tissue lacked
skin appendages. These choristomatous cutaneous tissues hindered normal
growth of ocular structures, resulting in microphthalmos. Use of computed
tomography was helpful in evaluating the extent of ocular tissue
involvement and accompanying intraocular malformations.
