Superior segmental optic hypoplasia. A sign of maternal diabetes
R. Y. Kim, W. F. Hoyt, S. Lessell and M. H. Narahara
Department of Neurological Surgery, School of Medicine, University of California, San Francisco 94143.
In a review of 10 patients with superior segmental optic nerve hypoplasia,
all of whom were the children of diabetic mothers, 17 of 20 eyes had one or
more of four characteristic findings in the optic disc: relative superior
entrance of the central retinal artery, pallor of the superior disc,
superior peripapillary halo, and thinning of the superior peripapillary
nerve fiber layer. We believe that the presence of these four signs of
superior segmental optic nerve hypoplasia strongly suggests maternal
diabetes.