High hyperopia in Leber's congenital amaurosis
R. S. Wagner, A. R. Caputo, L. B. Nelson and D. Zanoni
Few studies comment on the type of refractive errors found in patients with
Leber's congenital amaurosis. The association of an uncomplicated infantile
form of this condition with high hyperopia but without systemic
complications has been suggested. In a retrospective study, we identified
11 patients who satisfied the criteria for the diagnosis of this subtype of
Leber's congenital amaurosis. All of our cases were found to have at least
+6.00 diopters of hyperopia on cycloplegic refraction. No systemic
abnormalities were found in any of these children. We suggest that high
hyperopia be included in the diagnostic criteria of this specific form of
Leber's congenital amaurosis.
