Leber's idiopathic stellate neuroretinitis
R. F. Dreyer, G. Hopen, J. D. Gass and J. L. Smith
Twenty-nine eyes of 27 patients demonstrated the typical features of
neuroretinitis with a mascular star. Historical and fluorescein
angiographic features of this condition implicate a bloodborne infectious
agent. It is likely that multiple agents can produce this condition,
including the agent of cat-scratch fever and leptospirosis. A small
subgroup may exist in whom this condition resembles anterior ischemic optic
neuropathy and has a less favorable clinical course than is usual. There is
evidence that this condition is not related to demyelinating disease. It is
emphasized that this condition is not a maculopathy since vascular leakage
in the optic nerve causes the star. Therefore, we suggest that this
condition be renamed Leber's idiopathic stellate neuroretinitis.
